|
|
Line 4: |
Line 4: |
| |PDB= 1o1p |SIZE=350|CAPTION= <scene name='initialview01'>1o1p</scene>, resolution 1.80Å | | |PDB= 1o1p |SIZE=350|CAPTION= <scene name='initialview01'>1o1p</scene>, resolution 1.80Å |
| |SITE= | | |SITE= |
| |LIGAND= <scene name='pdbligand=HEM:PROTOPORPHYRIN IX CONTAINING FE'>HEM</scene> | | |LIGAND= <scene name='pdbligand=HEM:PROTOPORPHYRIN+IX+CONTAINING+FE'>HEM</scene> |
| |ACTIVITY= | | |ACTIVITY= |
| |GENE= | | |GENE= |
| | |DOMAIN= |
| | |RELATEDENTRY=[[1o1i|1o1i]], [[1o1j|1o1j]], [[1o1k|1o1k]], [[1o1l|1o1l]], [[1o1m|1o1m]], [[1o1n|1o1n]], [[1o1o|1o1o]] |
| | |RESOURCES=<span class='plainlinks'>[http://oca.weizmann.ac.il/oca-docs/fgij/fg.htm?mol=1o1p FirstGlance], [http://oca.weizmann.ac.il/oca-bin/ocaids?id=1o1p OCA], [http://www.ebi.ac.uk/pdbsum/1o1p PDBsum], [http://www.rcsb.org/pdb/explore.do?structureId=1o1p RCSB]</span> |
| }} | | }} |
|
| |
|
| '''Deoxy hemoglobin (A-GLY-C:V1M; B,D:V1M,C93A,N108K)''' | | '''Deoxy hemoglobin (A-GLY-C:V1M; B,D:V1M,C93A,N108K)''' |
|
| |
|
|
| |
| ==Disease==
| |
| Known diseases associated with this structure: Erythremias, alpha- OMIM:[[http://www.ncbi.nlm.nih.gov/entrez/dispomim.cgi?id=141800 141800]], Erythremias, beta- OMIM:[[http://www.ncbi.nlm.nih.gov/entrez/dispomim.cgi?id=141900 141900]], Erythrocytosis OMIM:[[http://www.ncbi.nlm.nih.gov/entrez/dispomim.cgi?id=141850 141850]], HPFH, deletion type OMIM:[[http://www.ncbi.nlm.nih.gov/entrez/dispomim.cgi?id=141900 141900]], Heinz body anemia OMIM:[[http://www.ncbi.nlm.nih.gov/entrez/dispomim.cgi?id=141850 141850]], Heinz body anemias, alpha- OMIM:[[http://www.ncbi.nlm.nih.gov/entrez/dispomim.cgi?id=141800 141800]], Heinz body anemias, beta- OMIM:[[http://www.ncbi.nlm.nih.gov/entrez/dispomim.cgi?id=141900 141900]], Hemoglobin H disease OMIM:[[http://www.ncbi.nlm.nih.gov/entrez/dispomim.cgi?id=141850 141850]], Hypochromic microcytic anemia OMIM:[[http://www.ncbi.nlm.nih.gov/entrez/dispomim.cgi?id=141850 141850]], Methemoglobinemias, alpha- OMIM:[[http://www.ncbi.nlm.nih.gov/entrez/dispomim.cgi?id=141800 141800]], Methemoglobinemias, beta- OMIM:[[http://www.ncbi.nlm.nih.gov/entrez/dispomim.cgi?id=141900 141900]], Sickle cell anemia OMIM:[[http://www.ncbi.nlm.nih.gov/entrez/dispomim.cgi?id=141900 141900]], Thalassemia, alpha- OMIM:[[http://www.ncbi.nlm.nih.gov/entrez/dispomim.cgi?id=141850 141850]], Thalassemia-beta, dominant inclusion-body OMIM:[[http://www.ncbi.nlm.nih.gov/entrez/dispomim.cgi?id=141900 141900]], Thalassemias, alpha- OMIM:[[http://www.ncbi.nlm.nih.gov/entrez/dispomim.cgi?id=141800 141800]], Thalassemias, beta- OMIM:[[http://www.ncbi.nlm.nih.gov/entrez/dispomim.cgi?id=141900 141900]]
| |
|
| |
|
| ==About this Structure== | | ==About this Structure== |
Line 20: |
Line 20: |
| [[Category: Protein complex]] | | [[Category: Protein complex]] |
| [[Category: Brucker, E A.]] | | [[Category: Brucker, E A.]] |
| [[Category: HEM]]
| |
| [[Category: blood substitute]] | | [[Category: blood substitute]] |
| [[Category: heme]] | | [[Category: heme]] |
| [[Category: oxygen delivery vehicle]] | | [[Category: oxygen delivery vehicle]] |
|
| |
|
| ''Page seeded by [http://oca.weizmann.ac.il/oca OCA ] on Thu Mar 20 13:04:29 2008'' | | ''Page seeded by [http://oca.weizmann.ac.il/oca OCA ] on Sun Mar 30 22:38:30 2008'' |